AB0758 TAKAYASU DISEASE IN JUVENILE FORM: ABOUT 11 CASES
نویسندگان
چکیده
Background Takayasu disease is a non-specific inflammatory vasculitis of the large and medium caliber arteries occurring during 2nd or 3rd decade. Attachment before age 20 rare. Methods This retrospective descriptive study including patients with aged less than years out series 109 between 1984 2022 in department internal medicine vascular surgery at CHU INB SINA Rabat. Results We identified 11 cases under sex ratio 1 man to 2. 6 woman (8 women/ 3 men) The mean was 17 ±2. 8 (12 - years). (45. 5%) had hypertension diagnosis, 10 (90. 9%) symptomatology type murmur (54. 5. %), pulse suppression (63. 6%), lameness. intermittent (36. 4%), no ischemia (23. 1%) one patient extravascular: headache, fever, altered general condition... Inflammatory syndrome present diagnosis our (72. 7%) Aortic involvement found 7 63%) predominantly due abdominal aorta (6 patients). 4 36. %) arterial damage. cerebral (27. 27%). most common disorders stenosis 7%), thickening 5%), thrombosis (9. aneurysm 1%). 54%) heart as part study. dominated by cardiomyopathies (4 cases), 2 valvulopathy, only case pericarditis. Associated two rhythm disturbances. 28%) stroke-type neurological disease, which accounted for 18. 75% (16 cases/109 cases) global 3%) blindness optic nerve TAKAYASU V 5 followed I 4%). Type II IV were each; have not been described any patients. All received corticosteroid therapy, 9 (81. 8%) initiated immunosuppressant adalimumab, five a. angioplasty and/ more surgeries, complicated restenosis. stunt artery aorto-abdominal fistula. Four had. relapses their evolution. also noted tuberculosis meningoencephalitis associated bilateral 16-year-old and. concepts coarctation non-dilated 12-year-old 18-year-old patient. Conclusion Our consistent literature illustrates seriousness juvenile takayasu combination severe ophthalmological. REFERENCES: NIL. Acknowledgements: Disclosure Interests None Declared.
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ژورنال
عنوان ژورنال: Annals of the Rheumatic Diseases
سال: 2023
ISSN: ['1468-2060', '0003-4967']
DOI: https://doi.org/10.1136/annrheumdis-2023-eular.2751